Department of Neurosurgery, Neurosciences Centre, All India Institute of Medical Sciences, Ansari Nagar, New Delhi 110 029, India.
J Clin Neurosci. 2010 Apr;17(4):460-3. doi: 10.1016/j.jocn.2009.08.010. Epub 2010 Feb 26.
We analyzed the records of 44 patients with moyamoya disease evaluated and treated at our Institute from 1998 until 2007. Out of 44 patients, 18 (41%) were in the paediatric age group and 26 (59%) were adults. Presentation was ischemic in 14 (32%) and hemorrhagic in 30 patients (68%). Revascularization was performed in 11 patients (five patients with ischemic presentation and six with hemorrhagic presentation): nine patients underwent indirect revascularization procedures only and two patients underwent indirect revascularization procedures and a combined superficial temporal artery-middle cerebral artery bypass. Thirty-six patients (81.8%) were available for follow-up. Out of 11 patients who underwent revascularization procedures, none had further hemorrhagic or ischemic episodes. Out of the 19 conservatively managed patients who were followed-up, seven (36.8%) developed new episodes of ischemia (n=2) or hemorrhage (n=5). In-hospital mortality was 6.8% (three patients), all of whom were in the hemorrhagic presentation group.
我们分析了 1998 年至 2007 年在我们研究所评估和治疗的 44 例 moyamoya 病患者的记录。44 例患者中，18 例（41%）为儿科年龄组，26 例（59%）为成人。14 例（32%）表现为缺血性，30 例（68%）为出血性。11 例（5 例缺血表现，6 例出血表现）患者进行了血运重建：9 例仅行间接血运重建，2 例行间接血运重建和颞浅动脉-大脑中动脉吻合术。36 例（81.8%）患者可进行随访。在接受血运重建的 11 例患者中，无一例发生进一步的出血或缺血事件。在 19 例接受保守治疗并随访的患者中，有 7 例（36.8%）出现新的缺血发作（2 例）或出血（5 例）。住院死亡率为 6.8%（3 例），均为出血组。
