Department of Gastroenterology and Hepatology, Mediterranean Institute for Transplantation and Advanced Specialized Therapies, University of Pittsburgh Medical Center, Via Tricomi 1, Palermo 90127, Italy.
World J Gastroenterol. 2010 Mar 7;16(9):1158-60. doi: 10.3748/wjg.v16.i9.1158.
Transjugular intrahepatic portosystemic shunt (TIPSS) is considered a valid therapeutic option for the treatment of portal hypertension and its complications. The guidelines for this procedure have already been established on the basis of the normal vascular anatomy and of various technical radiological aspects. In some few rare cases, diagnosis of a congenital vascular anomaly can be made accidentally by interventional radiologists, making the procedure of the TIPSS placement extremely difficult or in some cases technically impossible. This report describes a rare vascular malformation characterized by the absence of the right superior vena cava and persistence of the left superior vena cava in a patient with a diagnosis of advanced liver cirrhosis who needed a TIPSS placement in order to control refractory ascites.
经颈静脉肝内门体分流术（TIPSS）被认为是治疗门静脉高压及其并发症的有效治疗选择。该手术的指南已经根据正常的血管解剖结构和各种技术放射学方面建立起来。在少数罕见情况下，介入放射科医生偶然会诊断出先天性血管异常，这使得 TIPSS 放置的过程变得极其困难，或者在某些情况下从技术上是不可能的。本报告描述了一例罕见的血管畸形，其特征为右上腔静脉缺失和左上腔静脉持续存在，该患者患有晚期肝硬化，需要 TIPSS 放置以控制难治性腹水。
