Department of Pediatric Rheumatology, Princess Margaret Hospital for Children, Perth, WA, Australia.
Pediatr Rheumatol Online J. 2010 Jan 21;8:5. doi: 10.1186/1546-0096-8-5.
A 6 year old female with symptoms of small bowel obstruction underwent an exploratory laparotomy which revealed widespread evidence of inflammatory fibrotic adhesions involving the jejunal mesentery. In view of persistent growth failure, chronic anaemia, elevated acute phase reactants and imaging evidence of a diffuse progressive inflammatory process, the child was treated with corticosteroids and methotrexate with complete response. The literature on juvenile idiopathic sclerosing mesenteritis has been reviewed.
一位 6 岁女性因小肠梗阻症状接受了剖腹探查术,术中发现广泛的炎症性纤维粘连证据,累及空肠系膜。鉴于持续性生长发育不良、慢性贫血、急性期反应物升高和弥漫性进行性炎症过程的影像学证据,患儿接受了皮质类固醇和甲氨蝶呤治疗,获得完全缓解。对青少年特发性硬化性肠系膜炎的文献进行了回顾。