Division of Gastroenterology, Department of Medicine, Groote Schuur Hospital, Cape Town, South Africa.
Eur J Gastroenterol Hepatol. 2010 May;22(5):632-4. doi: 10.1097/MEG.0b013e328311a697.
The watery diarrhoea, hypokalaemia and achlorhydria syndrome is a rare cause of secretory diarrhoea. In this case report, we highlight a young female with watery diarrhoea, hypokalaemia and achlorhydria syndrome as a consequence of a vasoactive intestinal peptide producing composite adrenal phaeochromocytoma-ganglioneuroma. She made a complete recovery after curative surgical resection.
水样腹泻、低钾血症和胃酸缺乏综合征是一种罕见的分泌性腹泻病因。在本病例报告中,我们重点介绍了一名年轻女性,由于血管活性肠肽分泌复合性肾上腺嗜铬细胞瘤-神经节瘤导致水样腹泻、低钾血症和胃酸缺乏综合征。她在接受根治性手术切除后完全康复。