Caruana Maryanne, Grech Victor, Somerville Jane
Department of Cardiology, Mater Dei Hospital, Birkirkara Bypass, Birkirkara MSD2090, Malta.
Case Rep Med. 2010;2010:930589. doi: 10.1155/2010/930589. Epub 2010 Mar 9.
Hemianomalous pulmonary venous drainage with intact atrial septum is a rare congenital anomaly and reports of its surgical repair and the long-term complications related to the correction are only infrequently encountered in the literature. We report the case of a patient with hemianomalous pulmonary venous drainage and intact atrial septum who underwent surgical repair using a pericardial baffle and creation of an "atrial septal defect" aged 15 years. Dyspnoea and recurrent chest infections started 7 months after surgery when he was seen by a respiratory physician without cardiac followup. He presented again aged 28 years with a recurrent pneumonia investigated over 6 weeks and heart pronounced normal from examination and echocardiography. Correct diagnosis was made in Grown Up Congenital Heart (GUCH) clinic stimulating review of data and catheterisation with pulmonary artery angiography which confirmed it. We feel that this case highlights the importance of specialist care and followup for GUCH patients.
房间隔完整的半侧肺静脉异位引流是一种罕见的先天性畸形，其手术修复及与矫正相关的长期并发症的报道在文献中很少见。我们报告一例房间隔完整的半侧肺静脉异位引流患者，该患者15岁时接受了使用心包挡板的手术修复并制造了一个“房间隔缺损”。术后7个月，患者出现呼吸困难和反复肺部感染，当时呼吸科医生对其进行了诊治，未进行心脏随访。患者28岁时再次因反复肺炎就诊，经过6周的检查，体格检查和超声心动图显示心脏明显正常。在成人先天性心脏病（GUCH）诊所通过重新审查数据和进行肺动脉造影导管检查后做出了正确诊断，证实了病情。我们认为该病例凸显了对GUCH患者进行专科护理和随访的重要性。
