Resolution of tissue sphingomyelinase isoelectric profile in multiple components is extraction-dependent: evidence for a component defect in Niemann-Pick disease type C is spurious.

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作者信息

Harzer K, Anzil A P, Schuster I

出版信息

J Neurochem. 1977 Dec;29(6):1155-7. doi: 10.1111/j.1471-4159.1977.tb06525.x.

DOI:10.1111/j.1471-4159.1977.tb06525.x

PMID:202675

Abstract

摘要

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Resolution of tissue sphingomyelinase isoelectric profile in multiple components is extraction-dependent: evidence for a component defect in Niemann-Pick disease type C is spurious.

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