尼曼-匹克病。鞘磷脂酶缺乏症患者肝脏组织分析。 - Suppr

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Niemann-Pick disease. Analysis of liver tissue in sphingomyelinase-deficient patients.

作者信息

Elleder M, Smíd F, Harzer K, Cihula J

出版信息

Virchows Arch A Pathol Anat Histol. 1980;385(2):215-31. doi: 10.1007/BF00427406.

DOI:10.1007/BF00427406

PMID:7355571

Abstract

摘要

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Niemann-Pick disease: a review of eighteen patients.

Medicine (Baltimore). 1958 Feb;37(1):1-95. doi: 10.1097/00005792-195802000-00001.

Cephalinlipidosis; a new disorder of lipid metabolism.

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Adult lipidosis resembling Niemann-Pick's disease.

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Controlled chromation.

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Ceroid storage in a child with a Niemann-Pick type syndrome.

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[Augmentation of bis(monoacylglycerin)phosphric acid in sphingomyelinosis (M. Niemann-Pick?)].

Hoppe Seylers Z Physiol Chem. 1971 Feb;352(2):280-8. doi: 10.1515/bchm2.1971.352.1.280.

Two dimensional then layer chromatographic separation of polar lipids and determination of phospholipids by phosphorus analysis of spots.

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[Observations on the ultrastructure of lymph nodes in Niemann-Pick disease].

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