Department of Orthopaedics, Osaka University Graduate School of Medicine, Suita, Osaka, Japan.
Skeletal Radiol. 2010 Oct;39(10):1043-6. doi: 10.1007/s00256-010-0917-1. Epub 2010 Mar 23.
Kaposiform hemangioendothelioma (KHE) is a rare tumor that occurs nearly exclusively during infancy and childhood. It has features common to both capillary hemangioma and Kaposi sarcoma and for that reason many terms have been used for these tumors including "Kaposi-like infantile hemangioendothelioma" and "hemangioma with Kaposi sarcoma-like features." KHE typically presents as an ill-defined, red to purple, indurated plaque and is often complicated by the Kasabach-Merritt phenomenon (KMP), a condition of severe thrombocytopenia and consumptive coagulopathy. Knowledge of the radiological findings of this uncommon tumor might be helpful for diagnosis. We present the MRI features of a case of KHE with neither typical skin lesions nor the Kasabach-Merritt phenomenon.
卡波西样血管内皮细胞瘤(KHE)是一种罕见的肿瘤,几乎只发生在婴儿和儿童时期。它具有毛细血管血管瘤和卡波西肉瘤的共同特征,因此这些肿瘤有许多术语,包括“卡波西样婴儿血管内皮细胞瘤”和“具有卡波西肉瘤样特征的血管瘤”。KHE 通常表现为界限不清的红色至紫色硬结斑块,常伴有卡-梅现象(KMP),即严重血小板减少和消耗性凝血病。了解这种罕见肿瘤的放射学表现可能有助于诊断。我们报告了一例无典型皮肤病变和卡-梅现象的 KHE 的 MRI 特征。