Department of Nephrology, Ankara Numune Research and Education Hospital, Ankara, Turkey.
J Natl Med Assoc. 2010 Mar;102(3):247-9. doi: 10.1016/s0027-9684(15)30531-9.
We report a patient with medullary sponge kidney (MSK) who presented with hematuria and nephrotic-range proteinuria. Renal biopsy revealed a diagnosis of renal AA amyloidosis. No secondary factors contributing to renal amyloidosis were demonstrated. To the best of our knowledge, this is the first reported case that demonstrates the coexistence of MSK and renal AA amyloidosis.
我们报告了一例以血尿和肾病范围蛋白尿为表现的髓质海绵肾(MSK)患者。肾活检提示肾 AA 淀粉样变性的诊断。未发现导致肾淀粉样变性的其他继发因素。据我们所知,这是首例报道的同时存在 MSK 和肾 AA 淀粉样变性的病例。