Schiffmann J H, Rehder H, Speer C P
Universitäts-Kinderklinik Göttingen.
Monatsschr Kinderheilkd. 1991 Feb;139(2):102-4.
Tracheal agenesis is a rare congenital anomaly which presents immediately after birth an absolute respiratory insufficency. This report describes a new-born infant with a tracheal agenesis Typ II which was combined with an esophageal atresia and distal esophagotracheal fistula. In addition, costal synostosis was found. These malformations can be added to the VATER-association. Resuscitation of our patient (orotracheal and esophageal intubation, emergency coniotomy) was unsuccessful. However, in most cases of tracheal agenesis with esophagotracheal communication primary resuscitation is possible by esophageal intubation and by application of continuous positive pressure ventilation. Diagnosis must be confirmed by immediate contrast roentgenography or endoscopy. The results of surgery are disappointing until now.
气管缺如是一种罕见的先天性畸形,出生后立即出现绝对的呼吸功能不全。本报告描述了一名患有II型气管缺如的新生儿,该患儿合并食管闭锁及远端食管气管瘘。此外,还发现了肋骨融合。这些畸形可归入VATER综合征。对我们的患者进行复苏(经口气管插管和食管插管、紧急环甲膜切开术)未成功。然而,在大多数伴有食管气管相通的气管缺如病例中,通过食管插管和持续正压通气进行初步复苏是可行的。必须通过立即进行的造影X线检查或内镜检查来确诊。到目前为止,手术结果令人失望。