Sankaran K, Bhagirath C P, Bingham W T, Hjertaas R, Haight K
Pediatrics. 1983 May;71(5):821-3.
Two cases with unusual primitive foregut anomalies are described. Both children, born within 24 hours of each other, had complete tracheal atresia, proximal esophageal atresia, and distal tracheoesophageal fistula along with some minor anomalies; both needed immediate tracheostomy for adequate ventilation. At 15 months of age, both patients are thriving and developing normally with the exception of their speech. A review of the literature revealed no other survivors with this condition. Diagnosis of tracheal atresia should be kept in mind when a newborn infant exhibits respiratory distress without an audible cry associated with failure to advance the endotracheal tube beyond the vocal cords. An immediate tracheostomy can be lifesaving in these children.
本文描述了两例罕见的原始前肠异常病例。两名患儿出生时间相隔不到24小时,均患有完全性气管闭锁、近端食管闭锁、远端气管食管瘘以及一些轻微异常;两人均需要立即进行气管切开术以获得足够的通气。在15个月大时,两名患者除了说话能力外,均茁壮成长且发育正常。文献回顾显示,没有其他患有这种疾病的幸存者。当新生儿出现呼吸窘迫且没有可闻及的哭声,同时气管插管无法通过声带时,应考虑气管闭锁的诊断。立即进行气管切开术对这些患儿可能是救命的。