Emara A A, Gabr T A
MD Audiology Unit, ENT Department, Tanta University, Cairo, Egypt.
J Laryngol Otol. 2010 Sep;124(9):950-6. doi: 10.1017/S0022215110000630. Epub 2010 Apr 14.
Auditory neuropathy is a disorder characterised by preservation of outer hair cell function, with normal otoacoustic emissions and/or cochlear microphonics, but an absent or distorted auditory brainstem response.
This study aimed to objectively assess hearing thresholds in patients with auditory neuropathy, using the auditory steady state response.
Thirteen patients with auditory neuropathy and 15 normal hearing subjects were examined. Audiological evaluation included basic audiological tests, otoacoustic emissions, auditory brainstem response and auditory steady state response.
In the auditory neuropathy patients, the auditory brainstem response was absent in 11 patients, while the auditory steady state response was absent in only three.
The auditory steady state response may serve as a valuable objective measure for assessing the hearing threshold across different frequencies in patients with auditory neuropathy. We recommend that auditory steady state response be used to complete the evaluation of patients with auditory neuropathy.
听神经病是一种以外毛细胞功能保留为特征的疾病，耳声发射和/或耳蜗微音电位正常，但听觉脑干反应缺失或畸变。
本研究旨在使用听觉稳态反应客观评估听神经病患者的听阈。
对13例听神经病患者和15例听力正常的受试者进行检查。听力学评估包括基本听力学测试、耳声发射、听觉脑干反应和听觉稳态反应。
在听神经病患者中，11例患者听觉脑干反应缺失，但仅3例患者听觉稳态反应缺失 。
听觉稳态反应可作为评估听神经病患者不同频率听阈的有价值的客观指标。我们建议使用听觉稳态反应来完善对听神经病患者的评估。
