Thøstesen Lisbeth Marianne, Lassen Lissi Bank, Qvist Niels, Gupte Girish, Husby Steffen
Børneafdeling H, Odense Universitets-hospital, H.C. Andersen Børnehospital, DK-5000 Odense, Denmark.
Ugeskr Laeger. 2010 Mar 15;172(11):886-7.
A girl with extensive Hirschsprung's disease was operated, leaving her with a 35 cm short bowel. She received long-term parenteral nutrition through a central catheter. Progressive liver failure and intravenous access problems developed and at the age of 5.5 years she was transplanted in Birmingham with 270 cm small bowel, a reduced liver and pancreas. After the transplantation she received immunosuppressive medication, ursodeoxycholic acid and antibiotic prophylaxis. She is now well and on enteral nutrition, 32 months after the transplantation.
一名患有广泛性先天性巨结肠症的女孩接受了手术，术后剩余35厘米的短肠。她通过中心静脉导管接受长期肠外营养。随后出现了进行性肝功能衰竭和静脉通路问题，在5.5岁时于伯明翰接受了移植手术，移植了270厘米的小肠、部分肝脏和胰腺。移植术后，她接受了免疫抑制药物、熊去氧胆酸和抗生素预防治疗。移植32个月后，她现在情况良好，正在接受肠内营养。
