Haberland Catherine
The Chicago Medical School, Rosalind Franklin University, North Chicago, Illinois, USA.
Ideggyogy Sz. 2010 Mar 30;63(3-4):87-93.
Frontotemporal dementia is the second most common early onset dementia after Alzheimer disease. Frontotemporal dementias are a complex group of dementias. The clinical diagnosis can be perplexing because of concurring psychiatric and neurologic syndromes. Frontotemporal lobar degeneration, the underlying pathology, represents an emerging group of proteinopathies. Genetic factors play an important part in the etiologies of dementias. This article overviews current defining characteristics of frontotemporal dementias known also as frontotemporal lobar degenerations.
额颞叶痴呆是继阿尔茨海默病之后第二常见的早发性痴呆。额颞叶痴呆是一组复杂的痴呆症。由于同时存在精神和神经综合征，临床诊断可能会令人困惑。潜在的病理学——额颞叶变性，是一组新出现的蛋白病。遗传因素在痴呆症的病因中起着重要作用。本文概述了目前已知的额颞叶痴呆（也称为额颞叶变性）的定义特征。
