Sie T H, Weber W, Freling G, Galama J, Spaans F, Vles J
Department of Neurology, University Hospital Maastricht, The Netherlands.
Eur Neurol. 1991;31(2):94-9. doi: 10.1159/000116654.
The rare case of a 19-year-old man who suffered a fulminant course of 'subacute' sclerosing panencephalitis (SSPE) leading to death in 6 weeks from the onset of the first symptoms is described. This patient was part of the first reported SSPE cluster in the Netherlands, of which the other 3 patients died 2-6 years after diagnosis was made. In addition, a review of the literature on the rare occurrence of rapidly progressive SSPE was performed.
本文描述了一例罕见病例,一名19岁男性患“亚急性”硬化性全脑炎(SSPE),病情急骤,自首次出现症状起6周内死亡。该患者是荷兰首例报告的SSPE病例集群中的一员,该集群中的其他3例患者在确诊后2至6年死亡。此外,还对关于快速进展型SSPE罕见发生情况的文献进行了综述。