Karaca Mustafa, Akan Mithat, Silav Gokalp, Akoz Tayfun
Dr Lutfi Kirdar Kartal Education and Research Hospital, Plastic, Reconstructive and Aesthetic Surgery Clinic, Istanbul, Turkey.
J Craniofac Surg. 2010 May;21(3):816-8. doi: 10.1097/SCS.0b013e3181d87ba4.
Teratomas can occur in almost any region of the body and are the most common extragonadal germ cell childhood tumors. Immature teratomas in the head and neck region cause severe deformity and threat life because of several reasons. Imaging investigation (ultrasonography, computed tomography, magnetic resonance imaging) is of outmost importance for the diagnosis and preoperative planning, considering that the total surgical resection of the teratoma constitutes the treatment of choice. Untreated teratomas have mortality rates of 80% to 100%. In this study, a giant craniofacial immature teratoma having both intracranial and extracranial primary lesions is reported. As a conclusion, intracranial primary lesions should be kept in mind in extracranial head and neck immature teratoma cases.
畸胎瘤几乎可发生于身体的任何部位，是儿童期最常见的性腺外生殖细胞肿瘤。头颈部的未成熟畸胎瘤由于多种原因会导致严重畸形并危及生命。鉴于畸胎瘤的完整手术切除是首选治疗方法，影像学检查（超声、计算机断层扫描、磁共振成像）对于诊断和术前规划至关重要。未经治疗的畸胎瘤死亡率为80%至100%。在本研究中，报告了一例同时具有颅内和颅外原发性病变的巨大颅面未成熟畸胎瘤。总之，在颅外头颈部未成熟畸胎瘤病例中应考虑到颅内原发性病变。
