Greelish James P, Chatterjee Subhasis, Byrne John G
Vanderbilt Heart and Vascular Institute, Department of Cardiac Surgery, Vanderbilt University School of Medicine, Nashville, Tennessee 37232-8802, USA.
J Card Surg. 2010 Sep;25(5):519-21. doi: 10.1111/j.1540-8191.2010.01040.x.
Carney's complex is an autosomal dominant syndrome characterized by recurrent atrial myxomas with concurrent endocrinopathies and characteristic dermatologic features. We present the case of a woman who presented with a recurrent atrial myxoma after two previous resections for myxomas through median sternotomies. As a consequence, we utilized a minimally invasive right thoracotomy approach. We discuss the clinical and pathologic features of Carney complex and the importance of identifying individuals and families with this condition for treatment and counseling.
卡尼综合征是一种常染色体显性综合征,其特征为复发性心房黏液瘤,同时伴有内分泌病和特征性皮肤表现。我们报告了一例女性患者,她此前曾通过正中胸骨切开术进行过两次黏液瘤切除术,之后又出现了复发性心房黏液瘤。因此,我们采用了微创右胸切开术。我们讨论了卡尼综合征的临床和病理特征,以及识别患有这种疾病的个体和家庭对于治疗和咨询的重要性。