Tamura Yamato, Seki Toshio
Department of Cardiovascular Surgery, Nara Prefectural Mimuro Hospital, Ikoma-gun, Nara, Japan.
Ann Thorac Cardiovasc Surg. 2014;20 Suppl:882-4. doi: 10.5761/atcs.cr.13-00058. Epub 2013 Aug 30.
We report a case of Carney complex with massive right ventricular myxoma after two-time excision of a left atrial myxoma. The patient was a 45-year-old woman with pyrexia. She temporarily lost consciousness during examination, and echocardiography and computed tomography (CT) showed a massive tumor in the right ventricle. Loss of consciousness was determined to be caused by intracardiac obstruction of blood flow due to the tumor, and corrective surgery was performed. Pathological findings indicated myxoma with no malignancy. Myxomas are benign, but there is frequent recurrence of tumors associated with Carney complex. Because her myxomas were accompanied by unusual skin pigmentation, she was diagnosed with Carney complex. Carney complex has a high rate of myxoma recurrence, and often runs in families. In all cases, it is necessary to observe the patient's course closely.
我们报告一例在两次切除左心房黏液瘤后出现巨大右心室黏液瘤的卡尼综合征病例。患者为一名45岁发热女性。她在检查期间短暂失去意识，超声心动图和计算机断层扫描（CT）显示右心室有一个巨大肿瘤。意识丧失被确定为由肿瘤导致的心内血流梗阻引起，并进行了矫正手术。病理结果显示为无恶性的黏液瘤。黏液瘤是良性的，但与卡尼综合征相关的肿瘤常有复发。由于她的黏液瘤伴有不寻常的皮肤色素沉着，她被诊断为卡尼综合征。卡尼综合征黏液瘤复发率高，且常呈家族性发病。在所有病例中，密切观察患者病程很有必要。
