Destuynder R, Menget A, Destuynder O, Lassauge F, Amsallem D, Aubert D, Noir A
Services de Pédiatrie, CHU Saint-Jacques, Besançon.
Arch Fr Pediatr. 1991 Feb;48(2):119-22.
The authors report 2 cases of functional intestinal pseudo-obstruction in infancy associated with intestinal and urologic anomalies. In the first case many intestinal obstructions occurred from the age of 3 weeks and the boy was operated on at 14 months of age. A short small bowel and an intestinal malrotation were found at surgery; the alimentary canal was completely aperistaltic, and an ileostomy was performed. Further operations were carried out, for obstruction due to adhesions, and lastly to perform another ileostomy. An antenatal diagnosis of megacystis had been made with ultrasonography. In the second case, the pseudo-obstruction syndrome occurred at the age of 1 month, due to a volvulus of the small bowel with malrotation. A second operation, one month later because of lack of intestinal transit showed an aperistaltic bowel and a colostomy was performed. The intestinal continuity was set up again at the age of 9 months and a fractional feeding was started. A megacystis was found during urologic investigations. Growth is correct for both children at 3 years of age. A review of the literature allowed to list the most frequent digestive or extradigestive anomalies associated with this syndrome.
作者报告了2例婴儿期功能性肠道假性梗阻病例，这些病例伴有肠道和泌尿系统异常。在第一例中，从3周龄起就发生了多次肠梗阻，该男孩在14个月大时接受了手术。手术中发现小肠短且肠旋转不良；消化道完全无蠕动，遂行回肠造口术。因粘连导致梗阻又进行了进一步手术，最后再次行回肠造口术。产前超声检查诊断为巨膀胱。在第二例中，1个月大时因小肠扭转伴旋转不良出现假性梗阻综合征。1个月后因肠道无蠕动进行了第二次手术，行结肠造口术。9个月大时恢复肠道连续性并开始少量喂食。泌尿系统检查发现巨膀胱。两名儿童3岁时生长发育正常。文献回顾列出了与该综合征相关的最常见的消化或非消化异常。
