Răducanu Anca Maria, Păuna Mihaela, Feraru I V
Department of Pediatric Dentistry, Faculty of Dental Medicine, "Carol Davila" University of Medicine and Pharmacy, Bucharest, Romania.
Rom J Morphol Embryol. 2010;51(2):371-4.
This clinical report describes the oral rehabilitation of a 7-year-old male diagnosed with hypohidrotic ectodermal dysplasia and anodontia.
Ectodermal dysplasia (ED) comprises a large, heterogeneous group of inherited disorders, which are defined by primary defects in the development of two or more tissues derived from the embryonic ectoderm (skin, hair follicles, nails, teeth, sebaceous and sweat glands). Our patient exhibited the typical general and cranio-facial features of ED as well as emotional and behavioral problems. The patient presents only one conical primary central incisor.
The treatment was focused to improve his esthetic needs and oral functions and included the fabrication of removable prostheses and of an acrylic crown on the single tooth existing in his mouth, manufactured by an original simple method. Six months follow-up points out that restorative treatment provided psychosocial and functional comfort to the young boy.
This clinical report demonstrates the importance of the prosthodontic treatment for oral rehabilitation in children with ED. The partial and complete removable dentures associated with the acrylic crown can be a reversible and inexpensive method of treatment for ED patients.
本临床报告描述了一名7岁男性患少汗型外胚层发育不良伴无牙症的口腔修复情况。
外胚层发育不良(ED)是一大类遗传性疾病,其特征是源自胚胎外胚层的两种或更多组织(皮肤、毛囊、指甲、牙齿、皮脂腺和汗腺)发育存在原发性缺陷。我们的患者表现出ED典型的全身和颅面部特征以及情绪和行为问题。该患者仅长出一颗圆锥形乳中切牙。
治疗重点在于满足其美观需求并改善口腔功能,包括制作可摘义齿以及采用一种原始的简单方法为其口腔中现存的单颗牙齿制作丙烯酸冠。六个月的随访表明,修复治疗为这名小男孩提供了心理社会和功能方面的舒适感。
本临床报告证明了口腔修复治疗对患有ED的儿童进行口腔康复的重要性。与丙烯酸冠相关的局部和全口可摘义齿对于ED患者而言可能是一种可逆且廉价的治疗方法。