Department of Neurosurgery, West China Hospital, Sichuan University, Chengdu 610041, China.
J Zhejiang Univ Sci B. 2010 Jun;11(6):429-32. doi: 10.1631/jzus.B0900375.
Congenital spinal intradural arachnoid cyst associated with intrathoracic meningocele is very rare. We report a case in a 9-year-old Chinese boy who presented with a two-week history of progressive paraparesis and gait ataxia. Magnetic resonance imaging revealed that a dorsal intradural extramedullary cystic lesion extended from T1 to T5 and compressed the spinal cord. A left lateral intrathoracic meningocele pouch was found incidentally at the level of T1. The arachnoid cyst as well as meningocele was removed and the spinal cord compression was relieved. Arachnoid cyst was confirmed by histological examination. The patient recovered well postoperatively. This is the second report of such a case in the world according to the available literature. The take-home message for our case is that the surgical approach should be individualized, depending on the size and location.
先天性硬脊膜内蛛网膜囊肿合并胸内脑膜膨出非常罕见。我们报告了一例 9 岁中国男孩的病例,该男孩出现进行性双下肢无力和步态共济失调两周。磁共振成像显示,一个位于 T1 至 T5 的硬脊膜外髓内囊性病变延伸,并压迫脊髓。在 T1 水平意外发现左侧胸腔脑膜膨出囊。蛛网膜囊肿和脑膜膨出被切除,脊髓压迫得到缓解。组织学检查证实为蛛网膜囊肿。术后患者恢复良好。根据现有文献,这是世界上第二例此类病例报告。我们的病例提示手术方法应根据囊肿的大小和位置个体化选择。