Tsutsumi Y, Ohnaka M, Ohashi H, Murakami A, Takahashi M, Tanaka T
Department of Cardiovascular Surgery, Fukui Cardiovascular Center, Japan.
Nihon Kyobu Geka Gakkai Zasshi. 1991 Apr;39(4):447-51.
A 7-year-old girl, who was diagnosed as anomalous origin of right pulmonary artery from innominate artery associated with left sided unilateral pulmonary hypertension due to left patent ductus arteriosus, was reported. The right pulmonary artery had a stenotic segment of it's origin containing ductal tissue. Operation was performed without the aid of cardiopulmonary bypass. The continuity between main and right pulmonary arteries was established by a pericardial roll graft. The postoperative course was uneventful and she is very well three years after correction. To our knowledge, this is a very rare case with such combination of congenital anomalies as anomalous origin of right pulmonary artery and left sided unilateral pulmonary hypertension to be reported in the literature in Japan.
报告了一名7岁女孩，她被诊断为右肺动脉起自无名动脉伴左侧单侧肺动脉高压，病因是动脉导管未闭。右肺动脉起始处有一段狭窄节段，内含导管组织。手术在未使用体外循环的情况下进行。通过心包卷片移植建立了主肺动脉与右肺动脉之间的连续性。术后过程顺利，矫正三年后她情况良好。据我们所知，这是日本文献中报道的右肺动脉异常起源和左侧单侧肺动脉高压这种先天性异常组合的非常罕见的病例。
