冯雷克林霍增氏神经纤维瘤病伴原发性肺癌

Gupta K B, Kumar Vipul, Tandon Sanjeev, Gill Meenu

Department of TB and Respiratory Medicine, Pt .B. D. Sharma University of Health Sciences, Rohtak, Haryana, India.

Lung India. 2009 Oct;26(4):130-2. doi: 10.4103/0970-2113.56348.

von Recklinghausen neurofibromatosis (NF-1) is the most common inherited syndrome predisposing to neoplasia, particularly neural crest-derived tumors. However, lung malignancies reported in association with neurofibromatosis are sparse. We present a case of a 48-year-old man with NF-1 that manifested as carcinoma of lung, in order to discuss the linkage between these two entities.

冯雷克林霍增氏神经纤维瘤病（NF-1）是最常见的易患肿瘤的遗传性综合征，尤其是神经嵴来源的肿瘤。然而，与神经纤维瘤病相关的肺癌报道却很罕见。我们报告一例48岁患有NF-1的男性患者，其表现为肺癌，旨在探讨这两种疾病之间的联系。