Rusthoven Chad, Shames Murray L, Bui Marilyn M, Gonzalez Ricardo J
University of South Florida Health Science Center, Graduate Medical Education, Tampa, FL, USA.
Vasc Endovascular Surg. 2010 Jul;44(5):385-91. doi: 10.1177/1538574410369711. Epub 2010 Jun 10.
Primary malignant tumors of the aorta (PMTAs) are an extremely rare clinical entity. In most cases, the diagnosis is made either postmortem or late in the course of disease due to a low index of clinical suspicion and presenting symptoms that mimic far more common athero-embolic processes. Due to the intravascular origin of these tumors, peripheral and mesenteric embolic events represent a major source of morbidity and mortality. We present the first reported case of a patient with a diagnosed PMTA treated with an endovascular aortic stent for the purpose of embolic prophylaxis. The presentation, diagnosis, classification, and management of PMTAs in the world literature are also reviewed.
主动脉原发性恶性肿瘤（PMTAs）是一种极其罕见的临床病症。在大多数情况下，由于临床怀疑指数较低且呈现出与更为常见的动脉粥样硬化栓塞过程极为相似的症状，诊断往往在尸检时或疾病晚期才能做出。由于这些肿瘤起源于血管内，外周和肠系膜栓塞事件是发病和死亡的主要原因。我们报告了首例经诊断为PMTA的患者接受血管内主动脉支架置入术以预防栓塞的病例。同时还对世界文献中PMTAs的临床表现、诊断、分类及治疗进行了综述。
