Ouakaa-Kchaou A, Jebali S, Elloumi H, Gargouri D, Kochlef A, Romani M, Kilani A, Kharrat J, Ghorbel A
Service d'hépato-gastro-entérologie, hôpital Habib Thameur, 8, rue Ali Ben Ayed, Montfleury, 1008 Tunis, Tunisie.
Rev Med Interne. 2011 Feb;32(2):e21-2. doi: 10.1016/j.revmed.2010.03.459.
Dysphagia is a common complaint of patients with Sjogren's syndrome, but its mechanism remains a subject of controversy. The association of Sjogren's syndrome with Plummer-Vinson syndrome remains uncommon. We report a 56-year-old women who presented both disorders. The diagnosis of the Plummer-Vinson syndrome was based on the classic triad of dysphagia, iron-deficiency anaemia and oesophageal webs. The diagnosis of Sjogren's syndrome was based on the presence of three Fox criteria. This association should incite us to search for common immuno-genetic pathogenic factors between these two syndromes.
吞咽困难是干燥综合征患者的常见主诉,但其发病机制仍存在争议。干燥综合征与普卢默-文森综合征的关联并不常见。我们报告了一名同时患有这两种疾病的56岁女性。普卢默-文森综合征的诊断基于吞咽困难、缺铁性贫血和食管蹼这一经典三联征。干燥综合征的诊断基于三项福克斯标准。这种关联应促使我们寻找这两种综合征之间共同的免疫遗传致病因素。