Sahin Cem, Ozseker Burak, Rencuzogullari Ibrahim, Zeybek Arife
Department of Internal Medicine, Mugla University Medical Faculty, Mugla, Turkey.
BMJ Case Rep. 2014 Jan 22;2014:bcr2013202047. doi: 10.1136/bcr-2013-202047.
The Plummer-Vinson syndrome is a clinical syndrome characterised by dysphagia, web or webs in upper oesophagus and iron-deficiency anaemia. The syndrome is often seen in women of age 40-70 years and rarely in adolescents. Plummer-Vinson syndrome might be associated with malignancy, myeloproliferative disorder and autoimmune diseases including coeliac disease, rheumatoid arthritis and Sjögren syndrome. However, according to our literature search, there are no reports of such case associated with thorax deformity, cardiac pathology and ocular findings. We present a case of an 18-year-old boy with a rare presentation of this syndrome including pectus carinatum, exotropia and mitral valve prolapsus.
普卢默-文森综合征是一种临床综合征,其特征为吞咽困难、食管上段出现蹼或膈膜以及缺铁性贫血。该综合征常见于40至70岁的女性,青少年中罕见。普卢默-文森综合征可能与恶性肿瘤、骨髓增殖性疾病以及自身免疫性疾病相关,包括乳糜泻、类风湿性关节炎和干燥综合征。然而,根据我们的文献检索,尚无该综合征与胸廓畸形、心脏病变及眼部表现相关的病例报道。我们报告一例18岁男孩,该综合征表现罕见,包括鸡胸、外斜视和二尖瓣脱垂。