Sood Disha, Mohan Neelam, Singh Amanjeet, Buxi Tarvinder Bir Singh, Nundy Samiran, Soin Arvinder Singh
Department of Surgical Gastroenterology & Liver Transplantation, Sir Ganga Ram Hospital, New Delhi, India.
Pediatr Transplant. 2011 Nov;15(7):E135-8. doi: 10.1111/j.1399-3046.2010.01320.x. Epub 2010 Jun 27.
A 10-yr-old girl presented with a seven-month history of upper abdominal discomfort and weight loss. Physical examination revealed an abdominal lump in the right hypochondrium and epigastrium. Ultrasound examination and a computerized tomographic scan showed a large lobulated mass arising from segments I, 1V, and VIII of liver with arteriovenous shunting and multiple small masses in segments VI and VII. An initial diagnosis of hemangioendothelioma with metastasis was made elsewhere following which she received chemotherapy. She had persistent abdominal discomfort because of which she became dependent on narcotics. The patient had fever because of tumor necrosis and also developed peripheral neuropathy. Finally, owing to progressively worsening of symptoms, she underwent left lobe living donor liver transplantation. Histopathological examination showed the mass to be a cavernous hemangioma, and the patient is now well.
一名10岁女孩出现上腹部不适和体重减轻7个月的病史。体格检查发现右季肋部和上腹部有一腹部肿块。超声检查和计算机断层扫描显示，肝脏第I、IV和VIII段有一个大的分叶状肿块，伴有动静脉分流，第VI和VII段有多个小肿块。在其他地方初步诊断为血管内皮瘤伴转移，随后她接受了化疗。她因持续的腹部不适而对麻醉药品产生依赖。患者因肿瘤坏死而发热，还出现了周围神经病变。最后，由于症状逐渐恶化，她接受了左叶活体供肝移植。组织病理学检查显示肿块为海绵状血管瘤，患者目前情况良好。
