Tripathy Kalpalata, Mallik Rabinarayan, Mishra Aparajita, Misra Debiprasad, Rout Niranjan, Nayak Padmalaya, Samantray Sagarika, Rath Jayshree
Department of Pathology, S.C.B. Medical College, Cuttack, India.
Case Rep Neurol. 2010 Jun 1;2(2):69-73. doi: 10.1159/000315621.
Malignant peripheral nerve sheath tumor with rhabdomyoblastic differentiation, malignant triton tumor, has a rare incidence. We report such a case in a 40-year-old male who presented with a mass over the buttock. He was a previously diagnosed case of neurofibroma in the same area. Histomorphology supported by immunostaining with S-100 protein confirmed the diagnosis. Malignant triton tumor has a poor prognosis owing to its aggressive biological behavior. The fact that the presence of this tumor in the buttock region is extremely rare has prompted the authors to report this case.
伴有横纹肌母细胞分化的恶性周围神经鞘瘤,即恶性蝾螈瘤,发病率很低。我们报告了一例40岁男性病例,该患者臀部出现肿块。他之前在同一区域被诊断为神经纤维瘤。S-100蛋白免疫染色支持的组织形态学证实了诊断。恶性蝾螈瘤因其侵袭性生物学行为而预后不良。该肿瘤在臀部区域极为罕见这一事实促使作者报告此病例。