Livaditou A, Alexiou G, Floros D, Filippidis T, Dosios T, Bays D
Air Force and Veterans Administration General Hospital, Athens, Greece.
Pathol Res Pract. 1991 Mar;187(2-3):284-9. doi: 10.1016/S0344-0338(11)80785-5.
Epithelioid angiosarcoma is a rare tumor quite recently described. There is no accurate epidemiological study of this tumor. Among the internal organs, the liver is the one most frequently affected with angiosarcoma while there is no reference to the adrenal gland as a primary site. It is well known that the direct exposure to arsenicals (especially of vineyard cultivators) may be an important causative factor in the pathogenesis of the disease. A 59-year-old male vineyard cultivator with an epithelioid angiosarcoma of the right adrenal gland is described. The histologic characteristics as well as the immunohistochemical profile of the tumor are presented and the literature is briefly reviewed.
上皮样血管肉瘤是一种最近才被描述的罕见肿瘤。目前尚无关于该肿瘤准确的流行病学研究。在内脏器官中，肝脏是血管肉瘤最常累及的器官，而肾上腺作为原发部位未见相关报道。众所周知，直接接触砷剂（尤其是葡萄园种植者）可能是该病发病机制中的一个重要致病因素。本文描述了一名59岁患右肾上腺上皮样血管肉瘤的男性葡萄园种植者。介绍了该肿瘤的组织学特征及免疫组化表现，并对相关文献进行了简要综述。
