Department of Neurology, Instituto de Investigaciones Neurológicas Raúl Carrea (FLENI), Buenos Aires, Argentina.
Curr Neurol Neurosci Rep. 2010 Nov;10(6):459-66. doi: 10.1007/s11910-010-0139-x.
Syringobulbia is an uncommon condition, usually a late complication of syringomyelia. It has predilection for the dorsolateral region of the medulla leading to damage to vestibular nuclei and their connections, as well as to the descending sympathetic fibers. Oscillopsia, nystagmus, and Horner syndrome are frequent manifestations of syringobulbia. Oscillopsia may be a disturbing symptom for the patient, whereas Horner syndrome is usually an asymptomatic finding. MRI detection of syringomyelia has led to earlier treatment of syringomyelia and prevention of upward extension of the cavity. This probably explains why syringobulbia is less frequently encountered at present. We propose to describe the neuro-ophthalmologic symptoms and signs that may be observed in patients with syringobulbia and the mechanisms involved in their appearance.
延髓空洞症是一种不常见的疾病，通常是脊髓空洞症的晚期并发症。它偏爱延髓的背外侧区域，导致前庭核及其连接的损伤，以及下行交感纤维的损伤。眼球震颤、眼球震颤和霍纳综合征是延髓空洞症的常见表现。眼球震颤可能是患者的一个困扰症状，而霍纳综合征通常是无症状的发现。磁共振成像（MRI）检测到脊髓空洞症，导致对脊髓空洞症的早期治疗和防止空洞向上延伸。这可能解释了为什么目前延髓空洞症的发病率较低。我们建议描述可能在延髓空洞症患者中观察到的神经眼科症状和体征，以及其出现的机制。
