Taghipour Mousa, Derakhshan Nima, Ghaffarpasand Fariborz
Department of Neurosurgery, Shiraz University of Medical Sciences, Shiraz, Iran.
Neuroscience Research Center, Shiraz University of Medical Sciences, Shiraz, Iran.
Bull Emerg Trauma. 2014 Oct;2(4):166-9.
Syringobulbiais very rare condition defined as slit-like fluid cavity in the brain stem. Several conditions have been reported to be associated with syringobulbia including neoplasms, spinal cord traumas or lesions such as tethered cord, hind-brain herniation, infections such as meningitis and in isolation. Although post-traumatic syringomyelia has been wieldy described previously, traumatic brain injury has not been reported as the mechanism and etiology of isolated syringobulbia. We herein report a 24-year old man with previous history of severe traumatic brain injury who presented with recent onset inability to walk or coordinate movements, ataxia, dysphonia, dysarthria, bilateral third nerve palsy with fixed dilated pupils and eyes deviated outward and downward. He was further diagnosed to have isolated syringobulbia extending to upper pons and lower midbrain. Isolated post-traumatic syringobulbia is extremely rare condition presenting insidiously with cranial nerve palsies, ataxia and dysarthria.
延髓空洞症是一种非常罕见的疾病,定义为脑干中出现的裂隙样液腔。据报道,有几种情况与延髓空洞症相关,包括肿瘤、脊髓创伤或病变(如脊髓栓系)、后脑疝、感染(如脑膜炎)以及孤立出现的情况。虽然创伤后脊髓空洞症此前已有大量描述,但创伤性脑损伤作为孤立性延髓空洞症的机制和病因尚未见报道。我们在此报告一名24岁男性,既往有严重创伤性脑损伤史,近期出现行走或协调运动能力丧失、共济失调、发音困难、构音障碍、双侧动眼神经麻痹伴瞳孔固定散大以及双眼向外向下偏斜。他被进一步诊断为孤立性延髓空洞症,病变延伸至上脑桥和中脑下部。孤立性创伤后延髓空洞症是一种极其罕见的疾病,隐匿性地表现为颅神经麻痹、共济失调和构音障碍。