Yasumoto Mayumi, Katada Yoshiaki, Matsumoto Reiko, Adachi Akiko, Kaneko Koh
Departments of Radiology, Saitama Red Cross Hospital, 8-3-33, Kamiochiai, Chuo-ku, Saitama, Saitama, Japan.
J Med Case Rep. 2010 Aug 26;4:290. doi: 10.1186/1752-1947-4-290.
Soft-tissue perineuriomas are rare benign peripheral nerve sheath tumors in the subcutis of the extremities and the trunks of young patients. To our knowledge, this the first presentation of the computed tomography and magnetic resonance imaging of a soft-tissue perineurioma in the retroperitoneum with pathologic correlation.
A 63-year-old Japanese man was referred for assessment of high blood pressure. Abdominal computed tomography and magnetic resonance imaging showed a well-defined, gradually enhancing tumor without focal degeneration or hemorrhage adjacent to the pancreatic body. Tumor excision with distal pancreatectomy and splenectomy was performed, as a malignant tumor of pancreatic origin could not be ruled out. No recurrence has been noted in the 16 months since the operation. Pathologic examination of the tumor revealed a soft-tissue perineurioma of the retroperitoneum.
Although the definitive diagnosis of soft-tissue perineurioma requires biopsy and immunohistochemical reactivity evaluation, the computed tomography and magnetic resonance imaging findings described in this report suggest inclusion of this rare tumor in the differential diagnosis when such findings occur in the retroperitoneum.
软组织束状神经瘤是一种罕见的良性周围神经鞘瘤，多见于年轻患者四肢和躯干的皮下组织。据我们所知，本文首次展示了经计算机断层扫描（CT）和磁共振成像（MRI）检查，并与病理结果相关联的腹膜后软组织束状神经瘤。
一名63岁的日本男性因高血压前来接受评估。腹部CT和MRI显示，在胰体旁有一个边界清晰、渐进性强化的肿瘤，无局灶性变性或出血。由于不能排除胰腺来源的恶性肿瘤，遂进行了肿瘤切除并联合远端胰腺切除术和脾切除术。术后16个月未见复发。肿瘤的病理检查显示为腹膜后软组织束状神经瘤。
虽然软组织束状神经瘤的明确诊断需要活检和免疫组化反应性评估，但本报告中描述的CT和MRI表现提示，当腹膜后出现这些表现时，应将这种罕见肿瘤纳入鉴别诊断。
