Dokal I S, Deenmamode M, Lewis S M
Department of Haematology, Royal Postgraduate Medical School and Hammersmith Hospital, London, England.
Clin Lab Haematol. 1990;12(4):387-93. doi: 10.1111/j.1365-2257.1990.tb00350.x.
Eight patients (six with idiopathic thrombocytopenic purpura, one with immune pancytopenia, and one with autoimmune haemolytic anaemia), who had previously been splenectomized, were found to have splenunculi using radioactively labelled heat damaged autologous erythrocytes. In all patients the splenunculi were found to have significant 'splenic function'. However, there was a poor correlation between the size and the function of the splenunculi. Splenunculectomies were carried out in two patients. This led to a complete haematological remission in one patient and partial remission in the other. In three patients, where splenunculectomies could not be undertaken, the patients had to remain on significant doses of immunosuppressive therapy. In one patient complete remission was achieved using a course of immunosuppressive therapy alone and in the remaining two there was insufficient information to draw valid conclusions. Blood clearance kinetic studies of heat damaged erythrocytes were found to provide an accurate functional assessment of the splenunculi in all patients. However, the presence of a functional splenunculus was found to be the cause of disease relapse in only some patients. Therefore, the management of similar patients should perhaps be along the same lines as that at their initial presentation, that is, immunosuppressive therapy should be tried if they are not on any at the time of relapse, if they are already on it, then splenunculectomy should be done.
8例曾接受脾切除术的患者(6例患有特发性血小板减少性紫癜,1例患有免疫性全血细胞减少症,1例患有自身免疫性溶血性贫血),通过放射性标记的热损伤自体红细胞被发现存在副脾。在所有患者中,副脾均被发现具有显著的“脾脏功能”。然而,副脾的大小与功能之间的相关性较差。对2例患者实施了副脾切除术。这使得1例患者实现了完全血液学缓解,另1例患者部分缓解。在3例无法进行副脾切除术的患者中,这些患者不得不继续使用大剂量免疫抑制治疗。1例患者仅通过一个疗程的免疫抑制治疗即实现了完全缓解,其余2例患者因信息不足无法得出有效结论。热损伤红细胞的血液清除动力学研究被发现能为所有患者的副脾提供准确的功能评估。然而,仅在部分患者中发现功能性副脾是疾病复发的原因。因此,对于类似患者的管理或许应与初次就诊时的管理方式相同,即如果复发时未接受任何治疗,应尝试免疫抑制治疗;如果已经在接受免疫抑制治疗,则应进行副脾切除术。