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儿童颞下窝胎儿横纹肌瘤。

Fetal rhabdomyoma of the infratemporal fossa in children.

机构信息

Inserm U-587, ENT and Head and Neck Surgery Department, Armand-Trousseau Hospital, Paris, France.

出版信息

Eur Ann Otorhinolaryngol Head Neck Dis. 2010 Mar;127(1):30-2. doi: 10.1016/j.anorl.2010.02.008. Epub 2010 Mar 25.

DOI:10.1016/j.anorl.2010.02.008
PMID:20822754
Abstract

INTRODUCTION

Fetal rhabdomyomas are very rare benign tumors with infrequent head and neck involvement. We present the first report of a case of a 3-year-old child with an infratemporal fossa location.

MATERIAL AND METHODS

Case study.

DISCUSSION

Given the volume of the tumor and its difficult-to-access location, medical treatment associating methotrexate and Velbé(R) was proposed, but was not effective on the tumor volume after four courses. Surgical intervention via a combined intraoral and preauricular temporal approach allowed monoblock excision. There were no postoperative complications.

CONCLUSION

Medical treatment was unsuccessful. Surgical excision controlled the lesion with no recurrence since surgery. The main differential diagnosis is rhabdomyosarcoma.

摘要

简介

胎儿横纹肌肉瘤是一种非常罕见的良性肿瘤,很少累及头颈部。我们报告首例发生于颞下窝的 3 岁儿童病例。

材料与方法

病例研究。

讨论

鉴于肿瘤体积大且位置难以到达,我们提出了联合使用甲氨蝶呤和 Velbé®进行药物治疗的方案,但在四个疗程后对肿瘤体积没有效果。通过经口和耳前颞部联合入路的手术干预,实现了整块切除。术后无并发症。

结论

药物治疗无效。手术切除控制了病变,术后无复发。主要的鉴别诊断是横纹肌肉瘤。

相似文献

1
Fetal rhabdomyoma of the infratemporal fossa in children.儿童颞下窝胎儿横纹肌瘤。
Eur Ann Otorhinolaryngol Head Neck Dis. 2010 Mar;127(1):30-2. doi: 10.1016/j.anorl.2010.02.008. Epub 2010 Mar 25.
2
Rhabdomyosarcoma of the infratemporal fossa: diagnostic dilemmas and surgical management.
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Mali Med. 2010;25(3):49-52.
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Transzygomatic approach to tumours of the parasellar region. Technical note.经颧弓入路治疗鞍旁区域肿瘤。技术说明。
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Case records of the Massachusetts General Hospital. Weekly clinicopathological exercises. Case 4-2004. A nine-month-old boy with an orbital rhabdomyosarcoma.马萨诸塞州总医院病例记录。每周临床病理讨论。病例4 - 2004。一名患有眼眶横纹肌肉瘤的9个月大男孩。
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