Bilgiç A, Ozbarlas N, Ozkutlu S, Ozer S, Ozme S
Department of Cardiology, Hacettepe University, Ankara, Turkey.
Jpn Heart J. 1990 Nov;31(6):789-97. doi: 10.1536/ihj.31.789.
In this article, the clinical and epidemiological characteristics of 137 children with cardiomyopathy admitted to the Hacettepe Pediatric Cardiology Unit were studied and the prognosis was evaluated after a follow-up period of 24 +/- 5 months. It was found that the highest proportion of patients were residents of Ankara, followed by the Northern and the Central Anatolian regions, and consanguinity between their parents was more common than the proportion for Turkey as a whole. Most of the patients had dilated cardiomyopathy (78.9%) and the age at which symptoms appeared varied according to the type of cardiomyopathy. A high proportion of patients came to the hospital with complaints of dyspnea and a decrease in effort capacity. The most common findings on the physical examination were hepatomegaly and tachycardia. Electrocardiographic and echocardiographic evaluations were made for all patients and cardiac catheterization and endomyocardial biopsy were performed when necessary. The outcome was as follows: 34.5% improved, 45.7% remained stable, 9.5% deteriorated and 10.3% died.
在本文中，对哈杰泰佩儿科心脏病科收治的137例心肌病患儿的临床和流行病学特征进行了研究，并在24±5个月的随访期后评估了预后。结果发现，患者中比例最高的是安卡拉居民，其次是安纳托利亚北部和中部地区，其父母近亲结婚的情况比土耳其全国的比例更为常见。大多数患者患有扩张型心肌病（78.9%），症状出现的年龄因心肌病类型而异。很大一部分患者因呼吸困难和活动能力下降前来就诊。体格检查中最常见的发现是肝肿大和心动过速。对所有患者进行了心电图和超声心动图评估，并在必要时进行了心导管检查和心内膜活检。结果如下：34.5%好转，45.7%保持稳定，9.5%恶化，10.3%死亡。
