Dolara A, Cecchi F, Ciaccheri M
Servizio di Cardiologia, S. Luca, Ospedale di Careggi, Firenze.
G Ital Cardiol. 1989 Nov;19(11):1074-9.
Since the number of patients suffering from cardiomyopathy in Italy is unknown at present, a multicentre survey was carried out in 15 University and Hospital cardiological centres. Each centre was asked to report the number of cases of dilated, hypertrophic or restrictive cardiomyopathy observed between 1970 and 1987. Information was also sought regarding the residence of the patient at the time of diagnosis. Diagnostic criteria for each type of cardiomyopathy, based on those published in the current literature, were sent to the participating centres. For the entire period, a total of 2,229 patients with dilated, 913 with hypertrophic, and 64 with restrictive cardiomyopathy were reported. The number of cases observed between 1980-87 was about four times greater than that observed between 1970-79 for dilated cardiomyopathy and three times greater for hypertrophic cardiomyopathy. In the period 1970-79, a minimal annual incidence of dilated cardiomyopathies was calculated. In the centres this ranged from 0.005 to 1.8 per 100,000 inhabitants, although no systematic evaluation was made. On the contrary, minimal prevalence for hypertrophic cardiomyopathy ranged from 0.4 to 5.6 between 1970-79. These rates increased to 0.09-3.4 for dilated cardiomyopathy and to 1.0-23.0 for hypertrophic cardiomyopathy in the period 1980-87. On the basis of this survey the number of patients with a diagnosis of dilated and hypertrophic cardiomyopathy seems to be on the increase in our country. This increase may be due to the diagnostic facilities available, such as echocardiography, and possibly to a better knowledge and a greater interest in cardiomyopathies.(ABSTRACT TRUNCATED AT 250 WORDS)
由于目前意大利心肌病患者的数量未知,因此在15个大学和医院的心脏病中心开展了一项多中心调查。每个中心被要求报告1970年至1987年间观察到的扩张型、肥厚型或限制型心肌病的病例数。还收集了患者诊断时的居住地信息。基于当前文献中发表的诊断标准,将每种类型心肌病的诊断标准发送给参与中心。在整个时期,共报告了2229例扩张型心肌病患者、913例肥厚型心肌病患者和64例限制型心肌病患者。1980 - 1987年间观察到的扩张型心肌病病例数约为1970 - 1979年间的四倍,肥厚型心肌病为三倍。在1970 - 1979年期间,计算了扩张型心肌病的最低年发病率。在各中心,这一发病率每10万居民从0.005至1.8不等,尽管未进行系统评估。相反,1970 - 1979年间肥厚型心肌病的最低患病率在0.4至5.6之间。在1980 - 1987年期间,扩张型心肌病的这些发病率升至0.09 - 3.4,肥厚型心肌病升至1.0 - 23.0。基于这项调查,在我国,诊断为扩张型和肥厚型心肌病的患者数量似乎在增加。这种增加可能归因于现有的诊断设施,如超声心动图,也可能归因于对心肌病有了更好的了解和更大的关注度。(摘要截选至250词)