Intraventricular hemorrhage as an unusual presenting form of Sneddon syndrome.

BACKGROUND

Intraventricular hemorrhage, which has a poor prognosis, is an extremely rare presenting symptom of central nervous system vasculitis. Sneddon syndrome, which is a systemic vasculitic disease, generally presents with ischemic stroke and livedo reticularis. Intraventricular hemorrhage is extremely rare in Sneddon syndrome and has not been reported as the presenting complaint.

METHODS

We report a 37-year-old woman who presented with acute intraventricular hemorrhage, and on further evaluation her condition was diagnosed as Sneddon syndrome.

RESULTS

Patient underwent ventriculoperitoneal shunting operation for hydrocephalus and her condition markedly improved 6 months later; she was independent in her activities of daily living.

CONCLUSIONS

In this report, we emphasize the importance of multisystemic evaluation of patients, especially those with obscure angiography findings.