Konaş Ersoy, Tunçbilek Gökhan, Kayikçioğlu Aycan, Ozgür Figen
Department of Plastic Reconstructive and Aesthetic Surgery, Hacettepe University Medical School, Samanpazarı, Ankara, Turkey.
J Craniofac Surg. 2010 Sep;21(5):1645-7. doi: 10.1097/SCS.0b013e3181ef6b1f.
Congenital fusion of upper and lower jaw is rare. Only 35 bony syngnathia have been reported up to date, and 9 of them revealed posterior topography. A 10-day-old female infant with facial asymmetry, limited mouth opening, and cardiac murmurs is presented. The radiological findings revealed congenital bony fusion of right coronoid process of the mandible to posterior maxillary region and right palatal shelf agenesis of palatal bone, which seems to be the first case in the literature. Classification systems of bony syngnathia and applied treatment procedures for palatal closure and release of the bony fusion are discussed.
先天性上下颌融合较为罕见。迄今为止，仅报道过35例骨性颌骨融合病例，其中9例显示为后部融合。本文报告了一名10日龄的女婴，伴有面部不对称、张口受限及心脏杂音。影像学检查发现，该患儿右侧下颌冠状突与上颌后部区域先天性骨性融合，右侧腭骨腭突发育不全，这似乎是文献报道中的首例。本文还讨论了骨性颌骨融合的分类系统以及腭裂修复和骨性融合松解的应用治疗方法。
