Department of Autoimmune Diseases, Hospital Clínic-Institut d'Investigacions Biomèdiques Pi i Sunyer, Universitat de Barcelona, Spain.
Clin Exp Rheumatol. 2010 Jul-Aug;28(4 Suppl 60):S79-81. Epub 2010 Sep 24.
Behçet's disease is a systemic vasculitis characterised by recurrent mouth and genital ulcers and uveitis. About 25% of patients suffer from vascular involvement. We describe a patient with Behçet's disease who suffered recurrent pulmonary embolism and developed severe chronic thromboembolic pulmonary hypertension. The patient was successfully treated with pulmonary endarterectomy that normalised pulmonary haemodynamics. Chronic thromboembolic pulmonary hypertension is a potential complication of Behçet's disease that may be amenable to pulmonary endarterectomy.
白塞病是一种系统性血管炎，其特征为反复发作的口腔和生殖器溃疡以及葡萄膜炎。约 25%的患者存在血管受累。我们描述了 1 例白塞病患者，其反复发作肺栓塞并发展为严重的慢性血栓栓塞性肺动脉高压。患者接受肺动脉内膜剥脱术治疗后取得成功，肺血流动力学恢复正常。慢性血栓栓塞性肺动脉高压是白塞病的潜在并发症，可能适合肺动脉内膜剥脱术治疗。
