Márquez Galán F, López Roses L, Alfonso Bozzo M J, González-Gay Mantecón M A, Pérez Carnero A
Sección de Aparato Digestivo y Reumatología, Servicio de Medicina Interna, Hospital Xeral de Lugo.
Rev Esp Enferm Dig. 1990 Nov;78(5):311-3.
The association of primary biliary cirrhosis and a scleroderma of the CREST variation is called Reynold's syndrome. The case is presented of a 37 year old patient who appears with a digestive hemorrhage due to rupture of esophagel varices and who showed Raynaud phenomenon, sclerodactylia, positive anticentromere and antimitochondrial antibodies and a hepatic biopsy compatible with stage II of primary biliary cirrhosis.
原发性胆汁性肝硬化与CREST变异型硬皮病的关联被称为雷诺综合征。本文报告了一例37岁患者,该患者因食管静脉曲张破裂出现消化道出血,伴有雷诺现象、指端硬化、抗着丝点抗体和抗线粒体抗体阳性,肝脏活检结果符合原发性胆汁性肝硬化II期。