Dhaliwal Harmeet, McKaig Sarah
Leeds Dental Institute, UK.
Dent Update. 2010 Jul-Aug;37(6):364-6, 369-71. doi: 10.12968/denu.2010.37.6.364.
Dentinogenesis imperfecta (DI) is a hereditary condition which affects the development of dentine in both the primary and permanent dentitions. Three types of DI have been described in the literature. The presentation of DI is variable, depending on the type and severity of the disease. Early intervention in the treatment of a patient with DI is extremely important both for psycho-social and for functional reasons. This paper attempts to describe the clinical presentation and management of DI, and explores its association with certain medical conditions.
Recognition of DI is important, so that correct treatment principles may be instituted.
牙本质发育不全（DI）是一种遗传性疾病，会影响乳牙列和恒牙列中牙本质的发育。文献中描述了三种类型的DI。DI的表现因人而异，取决于疾病的类型和严重程度。出于心理社会和功能方面的原因，对DI患者进行早期干预治疗极为重要。本文试图描述DI的临床表现和管理，并探讨其与某些医学状况的关联。
认识DI很重要，以便能够制定正确的治疗原则。
