Macedo-Dias J A, Queiróz Machado F, Vouga L, Gonçalves V, Gomes R
Department of Pathology, Medical Faculty, University of Porto, Portugal.
Am J Cardiovasc Pathol. 1990;3(3):259-63.
The authors report a tumor of the heart in a 33-year-old man. Preoperative diagnosis was of a cardiac myxoma. Upon operation, the tumor was revealed to arise from the right atrial free wall, occupying most of the atrial and ventricular cavities and causing a noticeable enlargement and obstruction of the tricuspid valve as well as the mentioned cardiac chambers. A smaller part of the tumor was placed on the outside of the right atrial wall, and implants of the tumor in the distal part of the aorta, extending backward to the bifurcation of the pulmonary artery and its branches, were also observed. Histological examination showed a myxoid-type tumor with light and ultrastructural features of liposarcoma. The patient died 13 months after surgery with regional extension of the tumor.
作者报告了一名33岁男性的心脏肿瘤。术前诊断为心脏黏液瘤。手术中发现肿瘤起源于右心房游离壁,占据了大部分心房和心室腔,导致三尖瓣以及上述心脏腔室明显增大和梗阻。肿瘤的一小部分位于右心房壁外侧,还观察到肿瘤在主动脉远端有植入物,向后延伸至肺动脉及其分支的分叉处。组织学检查显示为黏液样型肿瘤,具有脂肪肉瘤的光镜和超微结构特征。患者术后13个月因肿瘤局部扩散死亡。