Pacor M L, Peroli P, Givanni S, Ambrosetti A, Biasi D, Bambara L M, Frigo A, Urbani G, Lunardi C
Istituto di Patologia Medica, Università, Verona, Italy.
Haematologica. 1990 Sep-Oct;75(5):470-2.
We describe a male patient with Behcet's syndrome and Castleman's lymphadenopathy. He was affected by severe oral and genital ulcers, bilateral uveitis, necrotic purulent nodules on both hands. A CT scan of the mediastinum showed the presence of a mediastinal mass. On the basis of histological and immunohistological findings, a diagnosis of Castleman's disease, angiofollicular type, was formulated. The lymphadenopathy was unicentric. After the surgical excision of the mediastinal mass (January, 1989) until now, Behcet's syndrome is in complete remission with a low dosage of prednisone.
我们描述了一位患有白塞氏综合征和Castleman淋巴结病的男性患者。他患有严重的口腔和生殖器溃疡、双侧葡萄膜炎以及双手坏死性脓性结节。纵隔CT扫描显示存在纵隔肿块。根据组织学和免疫组织学检查结果，确诊为血管滤泡型Castleman病。淋巴结病为单中心性。在手术切除纵隔肿块后（1989年1月）至今，白塞氏综合征在低剂量泼尼松治疗下完全缓解。
