Lipofibromatosis is a rare, benign fibrofatty tumor of childhood. Since the tumor was first characterized in 2000, only a few additional cases have been reported. The classic presentation of lipofibromatosis is a slow-growing mass arising in a distal extremity, with boys more commonly affected than girls. We report a 16-month-old girl who presented with a lipofibromatosis in her left scapular region that increased 30% in size during a 6-week period. Although previous case reports of lipofibromatosis have emphasized immunohistological findings, this paper focuses on imaging findings and discusses the utility of imaging in the differential diagnosis of pediatric soft-tissue tumors.