Yamahata Hitoshi, Hirahara Kazuho, Tomosugi Tetsuzo, Yamada Masahiko, Ishii Takeshi, Uetsuhara Koichi, Kawakami Kiyoshi, Arita Kazunori
Department of Neurosurgery, Kagoshima City Hospital, Kagoshima, Japan.
Neurol Med Chir (Tokyo). 2010;50(10):928-30. doi: 10.2176/nmc.50.928.
A 7-year-old girl with Glanzmann's thrombasthenia (GT) fell and hit her head against a table. Within 2 hours she began to vomit and became drowsy. On admission to our hospital her Glasgow Coma Scale score was 13. Computed tomography (CT) on admission showed acute epidural hematoma in the left posterior fossa. We administered platelets, performed emergent lateral suboccipital craniotomy, and totally removed the epidural hematoma. Postoperative CT showed no evidence of hematoma or re-bleeding. She was discharged without neurological deficits 14 days after the operation. GT is a platelet aggregation disorder due to a functional loss of platelet membrane glycoprotein IIb/IIIa. The present patient with GT underwent successful emergency craniotomy after platelet transfusion.
一名患有Glanzmann血小板无力症（GT）的7岁女孩摔倒，头部撞到桌子上。两小时内她开始呕吐并变得嗜睡。入院时格拉斯哥昏迷量表评分为13分。入院时计算机断层扫描（CT）显示左后颅窝急性硬膜外血肿。我们输注了血小板，进行了紧急枕下外侧开颅手术，并完全清除了硬膜外血肿。术后CT显示无血肿或再出血迹象。术后14天，她无神经功能缺损出院。GT是一种由于血小板膜糖蛋白IIb/IIIa功能丧失导致的血小板聚集障碍。本例GT患者在输注血小板后成功接受了急诊开颅手术。
