Messeguer F, Sanmartín O, Martorell-Calatayud A, Nagore E, Requena C, Guillén-Barona C
Servicio de Dermatología, Instituto Valenciano de Oncología, Valencia, España.
Actas Dermosifiliogr. 2010 Nov;101(9):792-7.
Acquired progressive lymphangioma is a rare vascular tumor with a locally aggressive behavior. Histologically it is characterized by a proliferation of numerous, dilated, thin-walled vessels lined by flat endothelial cells with no nuclear atypia. The vessels appear to dissect between the collagen fibers. It usually presents as an asymptomatic, slow-growing, reddish-brown plaque. We present the case of a 32-year-old man with acquired progressive lymphangioma. The tumor was in the hypogastric region and had arisen on a congenital vascular lesion previously diagnosed as multifocal cutaneous angiomatosis. It was very painful and impeded walking, for which reason it was decided to perform excision. Dermatologists and pathologists must be aware of acquired progressive lymphangioma as early surgical treatment, while the lesion is still small, is curative and prevents subsequent complications due to growth.
获得性进行性淋巴管瘤是一种罕见的血管肿瘤,具有局部侵袭性。组织学上,其特征是大量扩张的薄壁血管增生,血管内衬扁平内皮细胞,无核异型性。血管似乎在胶原纤维之间穿行。它通常表现为无症状、生长缓慢的红棕色斑块。我们报告一例32岁患有获得性进行性淋巴管瘤的男性病例。肿瘤位于下腹区域,发生于先前诊断为多灶性皮肤血管瘤病的先天性血管病变上。它非常疼痛,妨碍行走,因此决定进行切除。皮肤科医生和病理学家必须了解获得性进行性淋巴管瘤,因为早期手术治疗,即在病变仍较小的时候进行治疗,是可以治愈的,并可防止因肿瘤生长而导致的后续并发症。