Tungaria Arun, Srivastav Arun Kumar, Mahapatra Ashok K, Kumar Raj
Department of Neurosurgery, Sanjay Gandhi Post Graduate Institute of Medical Sciences, Lucknow, India.
J Pediatr Neurosci. 2010 Jan;5(1):52-4. doi: 10.4103/1817-1745.66677.
Congenital deformities involving the coverings of the nervous system are called neural tube defects (NTDs). NTD can be classified as neurulation defects, which occur by stage 12, and postneurulation defects. Cervical meningocele and myelomeningocele are rare spinal dysraphic lesions. Unlike lumbosacral dysraphic lesions, there is often no neurologic deficits and thus the subtle features of cervical cord tethering may be overlooked on imaging. The presence of meningomyelocele and/or encephaloceles at multiple (two or more) sites along the vertebral axis is a very rare event occurring in <1% of cases. Less than 10 cases have been described in the published literature. We are reporting a case of multiple NTD in same patient with no neurological deficit.
涉及神经系统被膜的先天性畸形称为神经管缺陷(NTDs)。NTD可分为在第12阶段之前发生的神经管形成缺陷和神经管形成后缺陷。颈段脑脊膜膨出和脊髓脊膜膨出是罕见的脊柱闭合不全性病变。与腰骶部脊柱闭合不全性病变不同,颈段病变通常没有神经功能缺损,因此在影像学检查中可能会忽略颈髓栓系的细微特征。沿脊柱轴在多个(两个或更多)部位出现脊髓脊膜膨出和/或脑膨出是一种非常罕见的情况,发生率不到1%。已发表的文献中描述的病例不到10例。我们报告了1例同一患者发生多处NTD但无神经功能缺损的病例。