Department of Biology and Biochemistry, University of Bath, Bath, United Kingdom BA2 7AY.
Metallomics. 2010 Mar;2(3):186-94. doi: 10.1039/b912601e. Epub 2009 Dec 4.
Neurodegenerative diseases include Alzheimer's and Parkinson's disease that are very common and other diseases that are notorious but occur less often such as Creutzfeldt-Jakob disease. In each case a protein is closely linked to the pathology of these diseases. These proteins include alpha-synuclein, the prion protein and Aβ. Despite first being discovered because of aggregates of these amyloidogenic proteins found in the brains of patients, these proteins all exist in the healthy brain where their normal function involves binding of metals. Recognition of these proteins as metalloproteins implies that the diseases they are associated with are possibly diseases with altered metal metabolism at their heart. This review considers the evidence that cell death in these diseases involves not just the aggregated proteins but also the metals they bind.
神经退行性疾病包括阿尔茨海默病和帕金森病,这些疾病非常常见,还有一些疾病比较罕见但也很著名,如克雅氏病。在每种情况下,一种蛋白质都与这些疾病的病理学密切相关。这些蛋白质包括α-突触核蛋白、朊病毒蛋白和 Aβ。尽管这些淀粉样蛋白聚集物最初是因为在患者大脑中发现而被发现的,但这些蛋白质都存在于健康的大脑中,它们的正常功能涉及金属的结合。将这些蛋白质识别为金属蛋白酶意味着它们所关联的疾病可能是其核心存在金属代谢改变的疾病。这篇综述考虑了这样一种证据,即在这些疾病中细胞死亡不仅涉及聚集的蛋白质,还涉及它们结合的金属。