Grover Patrick J, Jayaram Raja, Madder Hilary
Neurosciences Intensive Care Unit, West Wing, John Radcliffe Hospital, Headley Way, Headington, Oxford, UK.
Br J Neurosurg. 2010 Dec;24(6):684-5. doi: 10.3109/02688697.2010.500412.
We describe a case of cerebral venous thrombosis presenting in a patient with Lane-Hamilton syndrome and coeliac disease epilepsy cerebral calcification syndrome. This is a first reported occurrence of this combination. Delayed anticoagulation with early external ventricular drain insertion for life-threatening raised intracranial pressure resulted in a successful outcome.
我们描述了一例患有莱恩 - 汉密尔顿综合征和腹腔疾病癫痫性脑钙化综合征的患者出现脑静脉血栓形成的病例。这是首次报道的这种组合情况。对于危及生命的颅内压升高,延迟抗凝并早期插入外部脑室引流管,结果取得了成功。