Paksu Sule, Paksu Muhammet Sukru, Kalayci Ayhan Gazi, Sancak Recep
Department of Pediatrics, Ondokuz Mayys University Faculty of Medicine, Samsun, Turkey.
Indian Pediatr. 2012 Mar;49(3):243-4.
The combination of idiopathic pulmonary hemosiderosis (IPH) and celiac disease (CD) is rare. The clinical importance of this association is that a significant improvement can be obtained with gluten free diet not only in intestinal but also in pulmonary symptoms. A four and half-years old girl was admitted with complaints of cough, difficulty in breathing and paleness. She had intermittent episodes of abdominal pain and diarrhea. She had dyspnea and tachycardia, and oxygen saturation 88%. The patient was diagnosed with CD and concomitant IPH. With gluten-free diet and corticosteroid treatment, both intestinal and pulmonary symptoms were controlled.
特发性肺含铁血黄素沉着症(IPH)与乳糜泻(CD)合并存在的情况较为罕见。这种关联在临床上的重要意义在于,采用无麸质饮食不仅可使肠道症状,还能使肺部症状得到显著改善。一名四岁半的女童因咳嗽、呼吸困难和面色苍白入院。她有间歇性腹痛和腹泻。存在呼吸困难和心动过速,血氧饱和度为88%。该患者被诊断为乳糜泻合并特发性肺含铁血黄素沉着症。通过无麸质饮食和皮质类固醇治疗,肠道和肺部症状均得到了控制。